Brazilian Journal of Anesthesiology
https://bjan-sba.org/article/doi/10.1016/j.bjane.2021.10.013
Brazilian Journal of Anesthesiology
Case Report

Airway management in mucopolysaccharidosis: a retrospective case series review

Murat Tümer, Aysun Ankay Yılbaş, Sehend Debbağ, Fatma Sarıcaoğlu, Özgür Canbay

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Abstract

Airway management can be difficult in surgeries of patients with mucopolysaccharidosis. We performed a retrospective review of 31 surgeries performed between 2015 and 2019. The mean age of the patients was 127.6 months. MPS-IV and MPS-VI were the most frequent subtypes. Orthopedic surgeries were the most common surgery type. Difficult intubation was seen in 10 procedures. All patients with difficult intubation were aged over 36 months. Video laryngoscopy was the most common intubation method. Seventeen patients were followed up in the intensive care unit. Although video laryngoscopy seems to be a safe method in these patients, one should always be prepared for alternative methods.

Keywords

Airway management;  Difficult airway;  Mucopolysaccharidosis

References

1 J. Muenzer Overview of the mucopolysaccharidoses Rheumatology, 50 (2011), pp. v4-v12

2 BM Clark, J Sprung, TN Weingarten, et al. Anesthesia for patients with mucopolysaccharidoses: Comprehensive review of the literature with emphasis on airway management Bosn J Basic Med Sci, 18 (2018), pp. 1-7

3 A Moretto, MG Bosatra, L Marchesini, et al. Anesthesiological risks in mucopolysaccharidoses Italian journal of pediatrics, 44 (2018), pp. 47-55

4 P Arn, IA Bruce, JE Wraith, et al. Airway-related symptoms and surgeries in patients with mucopolysaccharidosis I Annals of Otology. Rhinology & Laryngology., 124 (2015), pp. 198-205

5 LU Madoff, A Kordun, JP. Cravero Airway management in patients with mucopolysaccharidoses: The progression toward difficult intubation Pediatric Anesthesia, 29 (2019), pp. 620-627
 

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