Brazilian Journal of Anesthesiology
https://bjan-sba.org/article/doi/10.1590/S0034-70942012000200013
Brazilian Journal of Anesthesiology
Clinical Information

Anestesia para lavagem pulmonar em paciente pediátrico portador de proteinose alveolar pulmonar

Anesthesia for lung lavage in pediatric patient with pulmonary alveolar proteinosis

Breno Monteiro Gonçalves; Vera Coelho Teixeira; Paulo Fernando Souto Bittencourt

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Resumo

JUSTIFICATIVA E OBJETIVOS: A proteinose alveolar pulmonar (PAP) é um transtorno raro, descrito inicialmente em 1958. A lavagem pulmonar total (LPT), proposta na década de 1960 ainda é o tratamento de escolha. Diversas técnicas foram descritas para realizar a lavagem pulmonar em pediatria, no entanto, todas apresentam limitações e riscos. RELATO DO CASO: Paciente de 6 anos e 8 meses, sexo feminino, 25 kg com o diagnóstico de proteinoise alveolar pulmonar submetida a lavagem pulmonar total por fibrobroncoscopia lobar sequencial sob anestesia geral em ventilação espontânea.

Palavras-chave

ANESTESIA, CIRURGIA, DOENÇAS RESPIRATÓRIAS, EQUIPAMENTOS, VENTILAÇÃO

Abstract

BACKGROUND AND OBJECTIVES: Pulmonary Alveolar Proteinosis (PAP) is a rare disorder first described in 1958. The Whole-Lung Lavage (WLL) proposed in the 1960s, remains the treatment of choice. Several techniques have been described to perform lung lavage in pediatric patients; however, all have limitation and risks. CASE REPORT: Female patient, aged 6 years and 8 months, 25 kg, diagnosed with pulmonary alveolar proteinoisis, who underwent whole-lung lavage by sequential lobar fiberoptic bronchoscopy under general anesthesia and spontaneous ventilation.

Keywords

Anesthesia, Bronchoscopy, Pediatrics, Pulmonary Alveolar Proteinosis, Ventilation

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