Resumo
JUSTIFICATIVA E OBJETIVOS: A associação de Vater é uma alteração politópica que inclui várias má-formações, sendo a hipoplasia radial a alteração mais freqüentemente encontrada ao nascimento. O objetivo deste relato é apresentar caso de associação de Vater em criança submetida a transplante renal. RELATO DO CASO: Paciente do sexo masculino, 11 anos, 23 kg, Hbs positivo submetido a esofagostomia com 30 horas de vida. Desde os 7 anos realiza hemodiálise, atualmente através de cateter atrial, por falta de outras vias de acesso. Submetido aos 11 anos a transplante renal com doador cadáver, sem intercorrências. Diurese adequada ao término das anastomoses vasculares. Drenagem de hematoma da fossa ilíaca D no primeiro dia de pós-operatório. Alta 21 dias após o transplante com função renal normal. CONCLUSÕES: A associação de Vater é uma ocorrência extremamente rara e complexa e o presente relato prende-se à realização, pela primeira vez, de transplante renal com doador cadáver em criança portadora desse defeito congênito, cujo resultado foi inteiramente satisfatório.
Palavras-chave
ANESTESIA, CIRURGIA, CIRURGIA, DOENÇAS
Abstract
BACKGROUND AND OBJECTIVES: Vater association is a polytopic disorder including several malformations of which radial hypoplasia is the most common observed at birth. This report aimed at describing a case of Vater association in a child submitted to renal transplantation. CASE REPORT: Male patient, 11 years old, 23 kg, Hbs positive, submitted to esophagostomy at 30 hours of life. Since 7 years of age patient is submitted to hemodialysis, currently via atrial catheter for the lack of other access ways. Renal transplantation with cadaver donor was performed without intercurrences with adequate diuresis after vascular anastomoses. Right iliac fossa hematoma was drained in the first postoperative day. Patient was discharged 21 days after transplantation with normal renal function. CONCLUSIONS: Vater association is an extremely rare and complex event and this report aimed at describing for the first time a renal transplantation with cadaver donor in a child with this congenital defect, the result of which has been fully satisfactory.
Keywords
ANESTHESIA, DISEASES, SURGERY, SURGERY
References
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