Brazilian Journal of Anesthesiology
https://bjan-sba.org/article/doi/10.1016/j.bjane.2021.02.045
Brazilian Journal of Anesthesiology
Case Report

Anesthetic management of a patient with type 1 neurofibromatosis and an occult pheochromocytoma: a case report

Polyxeni Theodosopoulou, K. Nastos, A. Paraskeva

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Abstract

Neurofibromatosis type 1 is a complex genetic disorder affecting multiple organ systems. Cardiovascular manifestations include hypertension, often associated with concomitant pheochromocytoma. We present a hypertensive crisis during induction of anesthesia in a patient with neurofibromatosis type 1, scheduled for abdominal myomectomy, which revealed an undiagnosed pheochromocytoma. The case highlights the importance of assessing all patients with neurofibromatosis type 1 for pheochromocytoma, because if it is left undiagnosed, it can be disastrous in the setting of anesthesia and surgery.

Keywords

Anesthetic management,  Pheochromocytoma,  NF-1,  Hypertensive crisis
60749a25a953956c7119f5b4 rba Articles
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Braz J Anesthesiol

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