Anesthetic management of a patient with type 1 neurofibromatosis and an occult pheochromocytoma: a case report
Polyxeni Theodosopoulou, K. Nastos, A. Paraskeva
http://dx.doi.org/10.1016/j.bjane.2021.02.045
Braz J Anesthesiol, Ahead of Print, 2021
Abstract
Neurofibromatosis type 1 is a complex genetic disorder affecting multiple organ systems. Cardiovascular manifestations include hypertension, often associated with concomitant pheochromocytoma. We present a hypertensive crisis during induction of anesthesia in a patient with neurofibromatosis type 1, scheduled for abdominal myomectomy, which revealed an undiagnosed pheochromocytoma. The case highlights the importance of assessing all patients with neurofibromatosis type 1 for pheochromocytoma, because if it is left undiagnosed, it can be disastrous in the setting of anesthesia and surgery.
Keywords
Anesthetic management,
Pheochromocytoma,
NF-1,
Hypertensive crisis