Brazilian Journal of Anesthesiology
https://bjan-sba.org/article/doi/10.1016/j.bjane.2016.01.002
Brazilian Journal of Anesthesiology
Clinical Information

Anesthesia in a child operated for cleft lip associated with Patau's syndrome

Anestesia em criança operada para lábio leporino associado à síndrome de Patau

Manoj Kamal; Don Varghese; Jeet Bhagde; Geeta Singariya; Annie Miju Simon; Amar Singh

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Abstract

Abstract Patients with Patau's syndrome (Trisomy 13) have multiple craniofacial, cardiac, neurological and renal anomalies with very less life expectancy. Among craniofacial anomalies cleft lip and palate are common. These craniofacial and cardiac anomalies present difficulties with anesthesia. We therefore describe the anesthetic management in the case of a Trisomy 13 child for operated for cleft lip at 10 months of age.

Keywords

Patau's syndrome, Cleft lip, Cleft palate, Paediatric anesthesia

Resumo

Resumo Os pacientes com síndrome de Patau (trissomia 13) apresentam várias anomalias craniofaciais, cardíacas, neurológicas e renais, com expectativa de vida bem menor. Entre as anomalias craniofaciais, o lábio leporino e a fenda palatina são comuns. Essas anomalias craniofaciais e cardíacas apresentam dificuldades na anestesia. Portanto, descrevemos o manejo anestésico em uma criança de 10 meses com trissomia 13 submetida à cirurgia de lábio leporino.

Palavras-chave

Síndrome de Patau, Lábio leporino, Fenda palatina, Anestesia pediátrica

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