Brazilian Journal of Anesthesiology
https://bjan-sba.org/article/doi/10.1016/j.bjane.2012.12.005
Brazilian Journal of Anesthesiology
Clinical Information

Anaesthesia for infant with Jarcho Levin syndrome: case report

Anestesia em criança com síndrome de Jarcho-Levin: relato de caso

Sukran Geze; Ufuk Arslan; Mustafa Tusat

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Abstract

ABSTRACTJarcho Levin syndrome is a rare disorder. There are various vertebral and costal anomalies. Severe deformities and abnormal fusion of ribs and vertebrae cause respiratory insufficiency and pneumonia. We present anaesthesia in a patient with Jarcho Levin syndrome for vesicoureteral reflux.

Keywords

Anaesthesia, infant, Jarcho Levin syndrome

Resumo

RESUMOA síndrome de Jarcho-Levin é um distúrbio raro que apresenta várias anomalias vertebrais e costais. Deformidades graves e fusões anormais das costelas e vértebras causam insuficiência respiratória e pneumonia. Apresentamos um caso de anestesia em paciente com síndrome de Jarcho-Levin para refluxo vesicuretral.

Palavras-chave

Anestesia, Criança, Síndrome de Jarcho-Levin

References

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